Redox susceptibility of SOD1 mutants is associated with the differential response to CCS over-expression in vivo

Neurobiology of Disease

Volumn 34, Issue 1, 2009, Pages 155-162

  Son, Marjatta ^a   Fu, Qiao ^a   Puttaparthi, Krishna ^a   Matthews, Christina M ^a   Elliott, Jeffrey L ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Amyotrophic lateral sclerosis; Cytochrome c oxidase; Mitochondria; Motor neuron; Paralysis; Transgenic

Indexed keywords

ALANINE; ARGININE; CHAPERONE; COPPER CHAPERONE FOR SOD1; COPPER ZINC SUPEROXIDE DISMUTASE; CYTOCHROME C OXIDASE; GLYCINE; LEUCINE; MONOMER; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; MOUSE; NONHUMAN; OXIDATION REDUCTION REACTION; PRIORITY JOURNAL; PROTEIN EXPRESSION; SPINAL CORD; SURVIVAL RATE;

ANIMALS; BLOTTING, WESTERN; ELECTRON TRANSPORT COMPLEX IV; IMMUNOHISTOCHEMISTRY; KAPLAN-MEIER ESTIMATE; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MITOCHONDRIA; MOLECULAR CHAPERONES; MUTATION; OXIDATION-REDUCTION; SPINAL CORD; SUPEROXIDE DISMUTASE;

EID: 62149091069     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2009.01.005     Document Type: Article

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