Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

Journal of Neuroscience

Volumn 18, Issue 9, 1998, Pages 3241-3250

  Kong, Jiming ^a   Xu, Zuoshang ^a  

^a UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

Author keywords

ALS; Degeneration; Mitochondria; Motor neuron; Paralysis; SOD1; Spinal cord

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL VACUOLE; CONTROLLED STUDY; DISEASE COURSE; MITOCHONDRION; MOTONEURON; MOUSE; MUSCLE ATROPHY; MUSCLE STRENGTH; NERVE CELL NECROSIS; NERVE DEGENERATION; NONHUMAN; PARALYSIS; PRIORITY JOURNAL; SPINAL CORD VENTRAL HORN;

EID: 0032079517     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.18-09-03241.1998     Document Type: Article

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