Mitochondrial respiratory chain dysfunction in muscle from patients with amyotrophic lateral sclerosis

Archives of Neurology

Volumn 67, Issue 7, 2010, Pages 849-854

  Crugnola, Veronica ^a   Lamperti, Costanza ^a   Lucchini, Valeria ^a   Ronchi, Dario ^a   Peverelli, Lorenzo ^a   Prelle, Alessandro ^a   Sciacco, Monica ^a   Bordoni, Andreina ^a   Fassone, Elisa ^a   Fortunato, Francesco ^a   Corti, Stefania ^a   Silani, Vincenzo ^a   Bresolin, Nereo ^a   Di Mauro, Salvatore ^b   Comi, Giacomo Pietro ^a   Moggio, Maurizio ^a  

^a UNIVERSITY OF MILAN   (Italy)

^b NewYork Presbyterian Hospital   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; DISEASE EXACERBATION; DISEASE SEVERITY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME DEFECT; FEMALE; GENE; GENE MUTATION; HISTOCHEMISTRY; HUMAN; HUMAN TISSUE; MAJOR CLINICAL STUDY; MALE; MITOCHONDRIAL RESPIRATORY CHAIN DYSFUNCTION; MUSCLE BIOPSY; MUSCLE CELL; PATHOGENESIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; RETROSPECTIVE STUDY; SKELETAL MUSCLE; SOD1 GENE; SOUTHERN BLOTTING; SPECTROPHOTOMETRY; SYMPTOM; TARDBP GENE;

ADULT; AGED; AMYOTROPHIC LATERAL SCLEROSIS; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; ELECTRON TRANSPORT COMPLEX IV; FEMALE; HUMANS; MALE; MIDDLE AGED; MITOCHONDRIA, MUSCLE; MITOCHONDRIAL DISEASES; SPECTROPHOTOMETRY; SUPEROXIDE DISMUTASE; YOUNG ADULT;

EID: 77955036882     PISSN: 00039942     EISSN: 15383687     Source Type: Journal    
DOI: 10.1001/archneurol.2010.128     Document Type: Article

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