Monomeric, oligomeric and polymeric proteins in huntington disease and other diseases of polyglutamine expansion

Brain Sciences

Volumn 4, Issue 1, 2014, Pages 91-122

  Hoffner, Guylaine ^a   Djian, Philippe ^a  

^a CNRS   (France)

Author keywords

Amyloid; Fibrils; Huntingtin; Huntington disease; Neurodegenerative diseases; Neuronal inclusions; Oligomers; Protein aggregation; Protein secondary structure; sheets

Indexed keywords

AMYLOID; HUNTINGTIN; MONOMERIC PROTEIN; OLIGOMERIC PROTEIN; PEPTIDES AND PROTEINS; POLYGLUTAMINE; POLYMERIC PROTEIN; PROTEINASE; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; BETA SHEET; BRAIN REGION; CARBOXY TERMINAL SEQUENCE; CELL INCLUSION; DEGENERATIVE DISEASE; DNA FLANKING REGION; HUMAN; HUNTINGTON CHOREA; NONHUMAN; PATHOGENESIS; POLYMERIZATION; PROTEIN AGGREGATION; PROTEIN POLYMORPHISM; PROTEIN SECONDARY STRUCTURE; REVIEW; SUMOYLATION; TOXICITY; UBIQUITINATION;

EID: 84913585530     PISSN: None     EISSN: 20763425     Source Type: Journal    
DOI: 10.3390/brainsci4010091     Document Type: Review

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