The Role of Protein Composition in Specifying Nuclear Inclusion Formation in Polyglutamine Disease

Journal of Biological Chemistry

Volumn 276, Issue 48, 2001, Pages 44889-44897

  Chai, Yaohui ^a   Wu, Lizi ^b   Griffin, James D ^b   Paulson, Henry L ^a  

^a UNIVERSITY OF IOWA   (United States)

^b BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

DISEASES;

INTRANUCLEAR COMPLEXES;

PROTEINS;

ATAXIN 3; CYCLIC AMP; NUCLEAR PROTEIN; POLYGLUTAMINE; PROTEIN DERIVATIVE; UNCLASSIFIED DRUG; E1A ASSOCIATED P300 PROTEIN; E1A-ASSOCIATED P300 PROTEIN; MJD1 PROTEIN; NERVE PROTEIN; PEPTIDE; TRANS ACTIVATORS; TRANSACTIVATOR PROTEIN;

AMINO ACID SEQUENCE; ARTICLE; CELL INCLUSION; CELL NUCLEUS INCLUSION BODY; DEGENERATIVE DISEASE; DENSITY GRADIENT; DNA RESPONSIVE ELEMENT; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; NERVE CELL DEGENERATION; NEUROTOXICITY; POLYGLUTAMINE DISEASE; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN INTERACTION; SPINOCEREBELLAR DEGENERATION; CELL FRACTIONATION; CELL NUCLEUS; CONFOCAL MICROSCOPY; FLUORESCENCE MICROSCOPY; GENETIC TRANSFECTION; GENETICS; HELA CELL; IMMUNOHISTOCHEMISTRY; METABOLISM; MUTATION; PLASMID; PROTEIN TERTIARY STRUCTURE; SERODIAGNOSIS;

ATAXIA;

CELL NUCLEUS; HELA CELLS; HUMAN; IMMUNOHISTOCHEMISTRY; MICROSCOPY, CONFOCAL; MICROSCOPY, FLUORESCENCE; MUTATION; NERVE TISSUE PROTEINS; NEURODEGENERATIVE DISEASES; NUCLEAR PROTEINS; PEPTIDES; PLASMIDS; PRECIPITIN TESTS; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; SUBCELLULAR FRACTIONS; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; TRANS-ACTIVATORS; TRANSFECTION;

EID: 0035976953     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M106575200     Document Type: Article

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