Hereditary dentatorubral-pallidoluysian atrophy: Detection of widespread ubiquitinated neuronal and glial intranuclear inclusions in the brain

Acta Neuropathologica

Volumn 96, Issue 6, 1998, Pages 547-552

  Hayashi, Yasuko ^a   Kakita, Akiyoshi ^a   Yamada, Mitsunori ^a   Koide, Reiji ^a   Igarashi, Shuichi ^a   Takano, Hiroki ^a   Ikeuchi, Takeshi ^a   Wakabayashi, Koichi ^a   Egawa, Shigekimi ^a   Tsuji, Shoji ^a   Takahashi, Hitoshi ^a  

^a NIIGATA UNIVERSITY   (Japan)

Author keywords

Dentatorubral pallidoluysian atrophy; Immunohistochemistry; Nuclear inclusion; Ubiquitin; Ultrastructure

Indexed keywords

ADENOSINE; ANTIBODY; CYTOSINE; GUANINE; POLYGLUTAMIC ACID; REPETITIVE DNA; UBIQUITIN;

ADULT; AGED; ARTICLE; ASTROCYTE; BRAIN NERVE CELL; CELL NUCLEUS INCLUSION BODY; CEREBELLUM CORTEX; CLINICAL ARTICLE; CONTROLLED STUDY; CORPUS STRIATUM; DENTATE NUCLEUS; DENTATORUBROPALLIDOLUYSIAN ATROPHY; ELECTRON MICROSCOPY; GENE; GLIA CELL; GRANULE CELL; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; INFERIOR OLIVE; PRIORITY JOURNAL; SPINAL CORD;

ADULT; AGED; BRAIN DISEASES; DENTATE GYRUS; GLOBUS PALLIDUS; HUMANS; INCLUSION BODIES; MIDDLE AGED; NEUROGLIA; NEURONS; RED NUCLEUS; UBIQUITINS;

EID: 0031739224     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010050933     Document Type: Article

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