Huntington's disease intranuclear inclusions contain truncated, ubiquitinated huntingtin protein

Experimental Neurology

Volumn 156, Issue 1, 1999, Pages 92-99

  Sieradzan, K A ^a   Mechan, A O ^b   Jones, L ^c   Wanker, E E ^d   Nukina, N ^e   Mann, D M A ^b  

^a MANCHESTER ROYAL INFIRMARY   (United Kingdom)

^b UNIVERSITY OF MANCHESTER   (United Kingdom)

^c CARDIFF UNIVERSITY   (United Kingdom)

^d MAX PLANCK INSTITUTE FOR MOLECULAR GENETICS   (Germany)

^e RIKEN BRAIN SCIENCE INSTITUTE   (Japan)

Author keywords

CAG trinucleotide repeats; Human brain; Huntingtin; Huntington's disease; Immunocytochemistry; Intranuclear inclusions; Molecular pathology

Indexed keywords

HUNTINGTIN; UBIQUITIN;

ADULT; AGED; ARTICLE; BRAIN CORTEX; CELL INCLUSION; CELL LOSS; CELLULAR DISTRIBUTION; CLINICAL ARTICLE; CORPUS STRIATUM; FEMALE; HUMAN; HUMAN TISSUE; HUNTINGTON CHOREA; IMMUNOCYTOCHEMISTRY; MALE; MORTALITY; NEUROTOXICITY; ONSET AGE; PRIORITY JOURNAL;

EID: 0033037919     PISSN: 00144886     EISSN: None     Source Type: Journal    
DOI: 10.1006/exnr.1998.7005     Document Type: Article

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