Ataxin-1 with an expanded glutamine tract alters nuclear matrix- associated structures

Nature

Volumn 389, Issue 6654, 1997, Pages 971-974

  Skinner, Pamela J ^a   Koshy, Beena T ^c   Cummings, Christopher J ^d   Klement, Ivan A ^a   Helin, Kara ^a   Servadio, Antonio ^e,g   Zoghbi, Huda Y ^c,e,f   Orr, Harry T ^a,b  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF MINNESOTA   (United States)

^c Prog in Cell and Molecular Biology ^*  (United States)

^d Molecular and Cellular Biology   (United States)

^e BAYLOR COLLEGE OF MEDICINE   (United States)

^f HOWARD HUGHES MEDICAL INSTITUTE   (United States)

^g TELETHON INSTITUTE OF GENETICS AND MEDICINE TIGEM   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 1; GENE PRODUCT; MUTANT PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL MODEL; ARTICLE; ATAXIA; CELLULAR DISTRIBUTION; CEREBELLUM DISEASE; DEGENERATIVE DISEASE; IMMUNOHISTOCHEMISTRY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PURKINJE CELL; SPINOCEREBELLAR DEGENERATION;

ANIMALS; BRAIN; COS CELLS; GLUTAMINE; HUMANS; IMMUNOHISTOCHEMISTRY; MICE; MICE, TRANSGENIC; MUTATION; NERVE TISSUE PROTEINS; NUCLEAR MATRIX; NUCLEAR PROTEINS; PURKINJE CELLS; SPINOCEREBELLAR DEGENERATIONS;

EID: 0030666001     PISSN: 00280836     EISSN: None     Source Type: Journal    
DOI: 10.1038/40153     Document Type: Article

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