Modelling biochemical features of mitochondrial neuropathology

Biochimica et Biophysica Acta - General Subjects

Volumn 1840, Issue 4, 2014, Pages 1380-1392

  Bird, Matthew J ^a,b   Thorburn, David R ^a,b   Frazier, Ann E ^a,b  

^a ROYAL CHILDREN'S HOSPITAL   (Australia)

^b UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

Cells; Mitochondrial disease; Mouse; Neuropathology

Indexed keywords

ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA; MITOCHONDRIAL RNA; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE;

BRAIN MITOCHONDRION; CALCIUM METABOLISM; CALCIUM SIGNALING; CELL VIABILITY; DISEASE ASSOCIATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA REPLICATION; FRIEDREICH ATAXIA; HUMAN; MITOCHONDRIAL MEMBRANE POTENTIAL; NEUROLOGIC DISEASE; NEUROPATHOLOGY; NONHUMAN; ORGANELLE SHAPE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PRIORITY JOURNAL; REVIEW; RNA PROCESSING;

ANIMALIA;

CELLS; MITOCHONDRIAL DISEASE; MOUSE; NEUROPATHOLOGY;

ANIMALS; BIOLOGICAL MARKERS; BRAIN DISEASES, METABOLIC; DISEASE MODELS, ANIMAL; DNA, MITOCHONDRIAL; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MODELS, NEUROLOGICAL; ORGANELLE SHAPE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS;

EID: 84895529040     PISSN: 03044165     EISSN: 18728006     Source Type: Journal    
DOI: 10.1016/j.bbagen.2013.10.017     Document Type: Review

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