Assembly of the oxidative phosphorylation system in humans: What we have learned by studying its defects

Biochimica et Biophysica Acta - Molecular Cell Research

Volumn 1793, Issue 1, 2009, Pages 200-211

  Fernández Vizarra, Erika ^a   Tiranti, Valeria ^a   Zeviani, Massimo ^a  

^a DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

Assembly; Electron transfer chain; Mitochondrial disorder; Mitochondrial DNA; Mitochondrial inner membrane; Mitochondrial respiratory chain; Oxidative phosphorylation; OXPHOS; Respiratory chain complex

Indexed keywords

ADENOSINE TRIPHOSPHATE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE;

HUMAN; MITOCHONDRIAL MEMBRANE; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN FUNCTION; RESPIRATORY CHAIN; REVIEW;

DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX III; ELECTRON TRANSPORT COMPLEX IV; HUMANS; MITOCHONDRIAL DISEASES; MODELS, BIOLOGICAL; MOLECULAR CHAPERONES; MUTATION; OXIDATIVE PHOSPHORYLATION;

EID: 56349124605     PISSN: 01674889     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbamcr.2008.05.028     Document Type: Review

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