The pathophysiology of mitochondrial disease as modeled in the mouse

Genes and Development

Volumn 23, Issue 15, 2009, Pages 1714-1736

  Wallace, Douglas C ^a   Fan, WeiWei ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Mitochondrial disease; Mitochondrion; Mouse model; mtDNA; OXPHOS dysfunction

Indexed keywords

MITOCHONDRIAL DNA; MITOCHONDRIAL PERMEABILITY TRANSITION PORE;

AGING; ANTIOXIDANT ACTIVITY; APOPTOSIS; BIOGENESIS; CAUSAL ATTRIBUTION; DEGENERATIVE DISEASE; ENERGY METABOLISM; GENE MUTATION; HUMAN; MALIGNANT NEOPLASTIC DISEASE; METABOLIC DISORDER; MITOCHONDRION; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; REVIEW;

ANIMALS; DISEASE MODELS, ANIMAL; ENERGY METABOLISM; GENES, MITOCHONDRIAL; HUMANS; MICE; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MUTATION; OXIDATIVE PHOSPHORYLATION; REACTIVE OXYGEN SPECIES;

MAMMALIA; MUS;

EID: 68149099553     PISSN: 08909369     EISSN: 15495477     Source Type: Journal    
DOI: 10.1101/gad.1784909     Document Type: Review

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