Mitochondrial disease in superoxide dismutase 2 mutant mice

Proceedings of the National Academy of Sciences of the United States of America

Volumn 96, Issue 3, 1999, Pages 846-851

  Melov, Simon ^a   Coskun, Pinar ^a   Patel, Manisha ^b   Tuinstra, Robbyn ^c   Cottrell, Barbara ^a   Jun, Albert S ^a   Zastawny, Tomsz H ^d   Dizdaroglu, Miral ^d   Goodman, Stephen I ^e   Huang, Ting Ting ^f   Miziorko, Henry ^c   Epstein, Charles J ^f   Wallace, Douglas C ^a  

^a EMORY UNIVERSITY   (United States)

^b NATIONAL JEWISH MEDICAL AND RESEARCH CENTER   (United States)

^c MEDICAL COLLEGE OF WISCONSIN   (United States)

^d NATIONAL INSTITUTE OF STANDARDS AND TECHNOLOGY   (United States)

^e Children's Hospital Colorado   (United States)

^f UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MUTANT PROTEIN; SUPEROXIDE DISMUTASE;

ARTICLE; CONTROLLED STUDY; ENZYME ANALYSIS; ENZYME DEFICIENCY; FRIEDREICH ATAXIA; GENE INACTIVATION; MITOCHONDRIAL MYOPATHY; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; RESPIRATORY CHAIN;

ACONITATE HYDRATASE; ANIMALS; BRAIN; CARBOXYLIC ACIDS; CROSSES, GENETIC; DNA DAMAGE; FEMALE; FUMARATE HYDRATASE; MALE; MICE; MICE, MUTANT STRAINS; MITOCHONDRIA; MITOCHONDRIA, HEART; MITOCHONDRIA, MUSCLE; MITOCHONDRIAL MYOPATHIES; OXIDATIVE PHOSPHORYLATION; OXO-ACID-LYASES; REACTIVE OXYGEN SPECIES; SUPEROXIDE DISMUTASE;

ATAXIA;

EID: 13044285432     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.96.3.846     Document Type: Article

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