Protein aggregation in motor neurone disorders

Neuropathology and Applied Neurobiology

Volumn 29, Issue 6, 2003, Pages 529-545

  Wood, J D ^a   Beaujeux, T P ^a   Shaw, P J ^a  

^a UNIVERSITY OF SHEFFIELD   (United Kingdom)

Author keywords

Aggregation; Amyotrophic lateral sclerosis; Androgen receptor; Polyglutamine; Spinobulbar muscular atrophy; Superoxide dismutase

Indexed keywords

ANDROGEN RECEPTOR; CHAPERONE; CYCLIC AMP RESPONSIVE ELEMENT BINDING PROTEIN BINDING PROTEIN; GLUTAMIC ACID; HEAT SHOCK PROTEIN; HYALIN; OLIGOMER; POLYGLUTAMINE; SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; BRAIN MITOCHONDRION; CELL CULTURE; CELL INCLUSION; CONTROLLED STUDY; CYTOSKELETAL DYSFUNCTION; CYTOSKELETON; DROSOPHILA; FAMILIAL DISEASE; GENE; GENE EXPRESSION; GENE MUTATION; GENETIC TRANSCRIPTION; GLUTAMATERGIC EXCITOTOXICITY; HUMAN; HUMAN CELL; HYALIN INCLUSION; HYALINE CONGLOMERATE INCLUSION; KENNEDY DISEASE; MITOCHONDRIAL DYSFUNCTION; MOTOR NEURON DISEASE; MOUSE; MOUSE MUTANT; NERVE CELL DEGENERATION; NERVE CELL NECROSIS; NERVE DEGENERATION; NERVE FIBER TRANSPORT; NEUROTOXICITY; NONHUMAN; OLIGOMERIZATION; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; PROTEIN MISFOLDING; REVIEW; SUPEROXIDE DISMUTASE 1 GENE; TRANSGENIC MOUSE; TRINUCLEOTIDE REPEAT; TRINUCLEOTIDE REPEAT EXPANSION DISORDER; UBIQUITINATED INCLUSION; X CHROMOSOME LINKED DISORDER;

ANIMALS; DISEASE MODELS, ANIMAL; HUMANS; INCLUSION BODIES; MOTOR NEURON DISEASE; MUTATION; PROTEIN CONFORMATION; PROTEINS; SUPEROXIDE DISMUTASE;

EID: 0346749654     PISSN: 03051846     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.0305-1846.2003.00518.x     Document Type: Review

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