Accumulation of wildtype and ALS-linked mutated VAPB impairs activity of the proteasome

PLoS ONE

Volumn 6, Issue 10, 2011, Pages

  Moumen, Anice ^a,b   Virard, Isabelle ^a,b   Raoul, Cédric ^a,b  

^a Turing Center for Living Systems CENTURI Aix Marseille University   (France)

^b AIX MARSEILLE UNIVERSITY   (France)

Author keywords

[No Author keywords available]

Indexed keywords

MEMBRANE PROTEIN; PROTEASOME; SALUBRINAL; UBIQUITIN; UNCLASSIFIED DRUG; VAPB PROTEIN; MUTANT PROTEIN; VAPB PROTEIN, HUMAN; VESICULAR TRANSPORT PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; CELL DEATH; CONJUGATION; CONTROLLED STUDY; CYTOPLASM; ENDOPLASMIC RETICULUM STRESS; HUMAN; MOTONEURON; NONHUMAN; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; UBIQUITINATION; WILD TYPE; ANIMAL; CELL STRAIN COS1; CERCOPITHECUS; CHEMISTRY; ENDOPLASMIC RETICULUM; GENE EXPRESSION REGULATION; GENETICS; METABOLISM; MUTATION; PROTEIN DEGRADATION; PROTEIN STABILITY; PROTEIN TRANSPORT;

PRIMATES;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CERCOPITHECUS AETHIOPS; COS CELLS; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; GENE EXPRESSION REGULATION; HUMANS; MUTANT PROTEINS; MUTATION; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN STABILITY; PROTEIN TRANSPORT; PROTEOLYSIS; UBIQUITIN; UBIQUITINATION; VESICULAR TRANSPORT PROTEINS;

EID: 80053594388     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0026066     Document Type: Article

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