Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading

Nature Neuroscience

Volumn 5, Issue 4, 2002, Pages 301-307

  Subramaniam, Jamuna R ^a   Lyons, W Ernest ^a   Liu, Jian ^b   Bartnikas, Thomas B ^c   Rothstein, Jeffrey ^a   Price, Donald L ^a   Cleveland, Don W ^b   Gitlin, Jonathan D ^c   Wong, Philip C ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHAPERONE; COPPER ION; NEUROFILAMENT PROTEIN; SUPEROXIDE DISMUTASE;

ALLELE; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; FACIAL NERVE; FAMILIAL DISEASE; GENE MUTATION; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NERVE FIBER TRANSECTION; NEUROFILAMENT; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; TISSUE HOMOGENATE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AXOTOMY; COPPER; HUMANS; LIFE EXPECTANCY; MICE; MICE, KNOCKOUT; MOLECULAR CHAPERONES; MOTOR NEURON DISEASE; MOTOR NEURONS; MUTATION; SPINAL CORD; SUPEROXIDE DISMUTASE; SURVIVAL RATE; TISSUE EXTRACTS;

EID: 0036212119     PISSN: 10976256     EISSN: None     Source Type: Journal    
DOI: 10.1038/nn823     Document Type: Article

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