Cell biology of spinocerebellar ataxia

Journal of Cell Biology

Volumn 197, Issue 2, 2012, Pages 167-177

  Orr, Harry T ^a  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; ATAXIN 1; ATAXIN 17; ATAXIN 3; ATAXIN 7; CYCLOHEXIMIDE; MUTANT PROTEIN; NUCLEIC ACID BINDING PROTEIN; POLYGLUTAMINE; PROTEASOME; PROTEINASE; SHORT HAIRPIN RNA; SILENCING MEDIATOR OF RETINOID AND THYROID HORMONE RECEPTOR; UBIQUITIN; UNCLASSIFIED DRUG; ATAXIN-1; NERVE PROTEIN; NUCLEAR PROTEIN; PEPTIDE; RBM17 PROTEIN, HUMAN; RNA BINDING PROTEIN;

ACTIN FILAMENT; BIOLOGICAL FUNCTIONS; CAG REPEAT; CELL FUNCTION; CELL STRUCTURE; CYTOPLASM; GENE INTERACTION; HUMAN; HUNTINGTON CHOREA; KENNEDY DISEASE; MACHADO JOSEPH DISEASE; MEMBRANE CHANNEL; MOTOR PERFORMANCE; NUCLEAR LOCALIZATION SIGNAL; PATHOGENESIS; PATHOGENICITY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN HOMEOSTASIS; PROTEIN INTERACTION; PROTEIN MOTIF; PROTEIN PHOSPHORYLATION; PURKINJE CELL; REVIEW; RNA METABOLISM; RNA SPLICING; SIGNAL TRANSDUCTION; SPINOCEREBELLAR DEGENERATION; SUMOYLATION; AMINO ACID SEQUENCE; CHEMISTRY; GENETICS; METABOLISM; PROTEIN SYNTHESIS; TRINUCLEOTIDE REPEAT;

AMINO ACID SEQUENCE; HUMANS; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PEPTIDES; PROTEIN BIOSYNTHESIS; RNA-BINDING PROTEINS; SIGNAL TRANSDUCTION; SPINOCEREBELLAR ATAXIAS; TRINUCLEOTIDE REPEAT EXPANSION; TRINUCLEOTIDE REPEATS;

EID: 84861943506     PISSN: 00219525     EISSN: 15408140     Source Type: Journal    
DOI: 10.1083/jcb.201105092     Document Type: Review

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