Evidence for proteasome involvement in polyglutamine disease: Localization to nuclear inclusions in SCA3/MJD and suppression of polyglutamine aggregation in vitro

Human Molecular Genetics

Volumn 8, Issue 4, 1999, Pages 673-682

  Chai, Yaohui ^a   Koppenhafer, Stacia L ^a   Shoesmith, Sarah J ^a   Perez, Matthew K ^b   Paulson, Henry L ^a  

^a UNIVERSITY OF IOWA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 3; GLUTAMINE; HYBRID PROTEIN; MUTANT PROTEIN; NERVE PROTEIN; PROTEASOME; PROTEASOME INHIBITOR; UNCLASSIFIED DRUG;

ANIMAL TISSUE; ARTICLE; BRAIN NERVE CELL; CELL NUCLEUS; CELL NUCLEUS INCLUSION BODY; CONTROLLED STUDY; DNA TRANSFECTION; ENZYME LOCALIZATION; HUMAN; HUMAN CELL; MACHADO JOSEPH DISEASE; NEWBORN; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; RAT;

ANIMALIA; ATAXIA;

EID: 0033030565     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/8.4.673     Document Type: Article

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