The polyglutamine neurodegenerative protein ataxin 3 regulates aggresome formation

Proceedings of the National Academy of Sciences of the United States of America

Volumn 102, Issue 12, 2005, Pages 4330-4335

  Burnett, Barrington G ^a   Pittman, Randall N ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Deubiquitinization; Proteasome; Protein aggregation; Spinocerebellar ataxia type 3 Machado Joseph disease; Ubiquitin interacting motif

Indexed keywords

ATAXIN 3; DYNEIN ADENOSINE TRIPHOSPHATASE; HISTONE DEACETYLASE; HISTONE DEACETYLASE 6; IODINE 125; LYSOZYME; MUTANT PROTEIN; POLYGLUTAMINE; PROTEASOME; SMALL INTERFERING RNA; TRANSMEMBRANE CONDUCTANCE REGULATOR; UBIQUITIN; UNCLASSIFIED DRUG;

AGGRESOME; ANIMAL CELL; ARTICLE; CONTROLLED STUDY; MACHADO JOSEPH DISEASE; MUTATION; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN BINDING; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN LOCALIZATION; PROTEIN TRANSPORT; UBIQUITINATION;

ANIMALS; BASE SEQUENCE; COS CELLS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DYNEIN ATPASE; HUMANS; INCLUSION BODIES; LYSINE; MACHADO-JOSEPH DISEASE; MICROTUBULES; MURAMIDASE; MUTATION; NERVE DEGENERATION; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN TRANSPORT; REPRESSOR PROTEINS; RNA, SMALL INTERFERING; UBIQUITIN;

ATAXIA;

EID: 15444372240     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0407252102     Document Type: Article

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