Recruitment of nonexpanded polyglutamine proteins to intranuclear aggregates in neuronal intranuclear hyaline inclusion disease

Journal of Neuropathology and Experimental Neurology

Volumn 60, Issue 4, 2001, Pages 369-376

  Takahashi, Junko ^a,e   Tanaka, Jinichi ^a   Arai, Kimihito ^b   Funata, Nobuaki ^c   Hattori, Takamichi ^b   Fukuda, Takahiro ^a   Fujigasaki, Hiroto ^d   Uchihara, Toshiki ^d  

^a JIKEI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b CHIBA UNIVERSITY   (Japan)

^c TOKYO METROPOLITAN KOMAGOME HOSPITAL   (Japan)

^d TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

^e PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

Author keywords

Ataxin; Intranuclear inclusions; Neurodegenerative disorder; Polyglutamine; Ubiquitin

Indexed keywords

ATAXIN 2; ATAXIN 3; POLYGLUTAMINE; PROTEASOME; PROTEIN; TATA BINDING PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG;

ADULT; ARTICLE; CASE REPORT; CELL NUCLEUS INCLUSION BODY; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DEGENERATIVE DISEASE; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOREACTIVITY; MALE; NERVE DEGENERATION; NEURONAL INTRANUCLEAR HYALINE INCLUSION DISEASE; NEUROPROTECTION; NUCLEAR LOCALIZATION SIGNAL; PATHOPHYSIOLOGY; PRIORITY JOURNAL;

EID: 0035060505     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1093/jnen/60.4.369     Document Type: Article

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