The polyglutamine expansion in spinocerebellar ataxia type 6 causes a β subunit-specific enhanced activation of P/Q-type calcium channels in Xenopus oocytes

Journal of Neuroscience

Volumn 20, Issue 17, 2000, Pages 6394-6403

  Restituito, Sophie ^a   Thompson, Randall M ^b   Eliet, Jacob ^a   Raike, Robert S ^b   Riedl, Maureen ^b   Charnet, Pierre ^a   Gomez, Christopher M ^b  

^a CNRS   (France)

^b UNIVERSITY OF MINNESOTA   (United States)

Author keywords

Calcium channel; Cerebellar ataxia; Channelopathy; Neurodegenerative disease; Polyglutamine tract; Purkinje cell; subunit

Indexed keywords

CALCIUM; CALCIUM CHANNEL; GUANINE NUCLEOTIDE BINDING PROTEIN; POLYGLUTAMINE;

ALPHA CHAIN; ANIMAL CELL; ARTICLE; BETA CHAIN; CHANNEL GATING; CHIMERA; CONTROLLED STUDY; DEGENERATIVE DISEASE; DENDRITE; GENE EXPRESSION; GENE MUTATION; GENETIC CODE; NERVE CELL DEGENERATION; NONHUMAN; PRIORITY JOURNAL; PURKINJE CELL; SPINOCEREBELLAR DEGENERATION; TRINUCLEOTIDE REPEAT; XENOPUS;

EID: 0034279182     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.20-17-06394.2000     Document Type: Article

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