The impairment of cholesterol metabolism in Huntington disease

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1851, Issue 8, 2015, Pages 1095-1105

  Leoni, Valerio ^a,b   Caccia, Claudio ^b  

^a OSPEDALE DI CIRCOLO   (Italy)

^b DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

Biomarker; Lipid; Mass spectrometry; Metabolomics; Neurodegeneration

Indexed keywords

24S HYDROXYCHOLESTEROL; 26 HYDROXYCHOLESTEROL; ABC TRANSPORTER G1; ABC TRANSPORTER G4; ACETYL COENZYME A; ADENOSINE TRIPHOSPHATE; APOLIPOPROTEIN E; CHOLESTEROL; CHOLESTEROL DERIVATIVE; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; LATHOSTEROL; LIVER X RECEPTOR; MEMBRANE PROTEIN; MYELIN BASIC PROTEIN; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; STEROL REGULATORY ELEMENT BINDING PROTEIN; UNCLASSIFIED DRUG; 24-HYDROXYCHOLESTEROL; HTT PROTEIN, HUMAN; LANOSTEROL; NERVE PROTEIN; ORPHAN NUCLEAR RECEPTOR;

BRAIN METABOLISM; CAG REPEAT; CHOLESTEROL BLOOD LEVEL; CHOLESTEROL METABOLISM; CHOLESTEROL SYNTHESIS; CHOLESTEROL TRANSPORT; DISEASE COURSE; DISORDERS OF CHOLESTEROL METABOLISM; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENOMICS; HUMAN; HUNTINGTON CHOREA; LIPID METABOLISM; METABOLOMICS; NERVE CELL; NONHUMAN; OLIGODENDROGLIA; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVIEW; TURNOVER TIME; UPREGULATION; ANIMAL; BRAIN CORTEX; CORPUS STRIATUM; GENE EXPRESSION REGULATION; GENETICS; METABOLISM; MOUSE; MUTATION; PATHOLOGY; TRINUCLEOTIDE REPEAT;

MURINAE;

ANIMALS; CEREBRAL CORTEX; CHOLESTEROL; CORPUS STRIATUM; GENE EXPRESSION REGULATION; HUMANS; HUNTINGTON DISEASE; HYDROXYCHOLESTEROLS; LANOSTEROL; MICE; MUTATION; NERVE TISSUE PROTEINS; ORPHAN NUCLEAR RECEPTORS; STEROL REGULATORY ELEMENT BINDING PROTEINS; TRINUCLEOTIDE REPEATS;

EID: 84930046200     PISSN: 13881981     EISSN: 18792618     Source Type: Journal    
DOI: 10.1016/j.bbalip.2014.12.018     Document Type: Review

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