Shaping the role of mitochondria in the pathogenesis of Huntington's disease

EMBO Journal

Volumn 31, Issue 8, 2012, Pages 1853-1864

  Costa, Veronica ^a   Scorrano, Luca ^a  

^a UNIVERSITY OF GENEVA   (Switzerland)

Author keywords

fusion fission; Huntington's disease; mitochondria; ultrastructure

Indexed keywords

ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATE; CALCIUM ION; CREATINE PHOSPHATE; GLUCOSE; GLUTAMATE RECEPTOR; HUNTINGTIN; LACTIC ACID; PHOSPHATE; PYRUVIC ACID;

APOPTOSIS; BASAL GANGLION; BIOENERGY; BRAIN CORTEX; BRAIN METABOLISM; CAG REPEAT; CELL DAMAGE; CELL FUNCTION; CELL STRUCTURE; CORPUS STRIATUM; DISEASE ASSOCIATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENERGY METABOLISM; GLUCOSE INTAKE; GLUCOSE TRANSPORT; HETEROZYGOTE; HUMAN; HUNTINGTON CHOREA; INBORN ERROR OF METABOLISM; LYMPHOBLASTOID CELL; MITOCHONDRION; MUSCLE METABOLISM; NONHUMAN; OXIDATIVE STRESS; PATHOGENESIS; PRIORITY JOURNAL; RESPIRATORY CHAIN; REVIEW; WEIGHT REDUCTION;

ANIMALS; BRAIN; DISEASE MODELS, ANIMAL; HUMANS; HUNTINGTON DISEASE; MITOCHONDRIA;

ANIMALIA;

EID: 84859904873     PISSN: 02614189     EISSN: 14602075     Source Type: Journal    
DOI: 10.1038/emboj.2012.65     Document Type: Review

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