Mitochondrial respiratory chain complex activity and bioenergetic alterations in human platelets derived from pre-symptomatic and symptomatic huntington's disease carriers

Mitochondrion

Volumn 13, Issue 6, 2013, Pages 801-809

  Silva, Ana C ^a   Almeida, Sandra ^a   Laço, Mário ^a   Duarte, Ana I ^a   Domingues, Joana ^b   Oliveira, Catarina R ^a,c   Januário, Cristina ^b,c   Rego, A Cristina ^a,c  

^a UNIVERSITY OF COIMBRA   (Portugal)

^b CENTRO HOSPITALAR E UNIVERSITÁRIO DE COIMBRA   (Portugal)

^c UNIVERSITY OF COIMBRA   (Portugal)

Author keywords

Adenine nucleotides; Huntington disease; Mitochondria; Mitochondrial respiratory chain complexes; Mutant huntingtin; Platelet

Indexed keywords

CITRATE SYNTHASE; CYTOCHROME C OXIDASE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIQUINOL CYTOCHROME C REDUCTASE;

ADULT; AGED; ARTICLE; ASYMPTOMATIC DISEASE; BIOENERGY; CAG REPEAT; CLINICAL ARTICLE; CONTROLLED STUDY; DISEASE CARRIER; ENZYME ACTIVITY; FEMALE; HUMAN; HUMAN CELL; HUNTINGTON CHOREA; MALE; MITOCHONDRIAL RESPIRATION; PRIORITY JOURNAL; RESPIRATORY CHAIN; THROMBOCYTE;

ADENINE NUCLEOTIDES; HUNTINGTON DISEASE; MITOCHONDRIA; MITOCHONDRIAL RESPIRATORY CHAIN COMPLEXES; MUTANT HUNTINGTIN; PLATELET;

ADULT; BLOOD PLATELETS; ELECTRON TRANSPORT; ENERGY METABOLISM; FEMALE; HETEROZYGOTE; HUMANS; HUNTINGTON DISEASE; MALE; MIDDLE AGED; MITOCHONDRIA;

EID: 84887018742     PISSN: 15677249     EISSN: 18728278     Source Type: Journal    
DOI: 10.1016/j.mito.2013.05.006     Document Type: Article

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