Towards a structural understanding of Friedreich's ataxia: Solution structure of frataxin

Structure

Volumn 8, Issue 7, 2000, Pages 695-707

  Musco, Giovanna ^a   Stier, Gunter ^b   Kolmerer, Bernhard ^b   Adinolfi, Salvatore ^a   Martin, Stephen ^a   Frenkiel, Tom ^a   Gibson, Toby ^b   Pastore, Annalisa ^a  

^a NATIONAL INSTITUTE FOR MEDICAL RESEARCH   (United Kingdom)

^b EUROPEAN MOLECULAR BIOLOGY LABORATORY   (Germany)

Author keywords

Iron metabolism; Mitochondrial disease; Neurodegenerative diseases; Nuclear magnetic resonance; Protein structure

Indexed keywords

FRATAXIN; IRON; IRON BINDING PROTEIN;

AMINO ACID SEQUENCE; AMINO TERMINAL SEQUENCE; ARTICLE; CARBOXY TERMINAL SEQUENCE; FRIEDREICH ATAXIA; HUMAN; IRON METABOLISM; NERVE CELL NECROSIS; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN STRUCTURE; STRUCTURE ANALYSIS;

ATAXIA;

EID: 0034661480     PISSN: 09692126     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0969-2126(00)00158-1     Document Type: Article

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