Deficit of in vivo mitochondrial ATP production in patients with Friedreich ataxia

Proceedings of the National Academy of Sciences of the United States of America

Volumn 96, Issue 20, 1999, Pages 11492-11495

  Lodi, Raffaele ^a,b,e   Cooper, J Mark ^c   Bradley, Jane L ^c   Manners, David ^a   Styles, Peter ^a   Taylor, Doris J ^a   Schapira, Anthony H V ^c,d  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b UNIVERSITY OF BOLOGNA   (Italy)

^c ROYAL FREE AND UNIVERSITY COLLEGE MEDICAL SCHOOL   (United Kingdom)

^d UNIVERSITY COLLEGE LONDON   (United Kingdom)

^e UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; FRATAXIN; IRON; MITOCHONDRIAL DNA;

ADOLESCENT; ADULT; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CHROMOSOME 9Q; CONTROLLED STUDY; DEGENERATIVE DISEASE; FEMALE; FRIEDREICH ATAXIA; HUMAN; HUMAN TISSUE; MALE; MITOCHONDRION; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; SKELETAL MUSCLE;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ADENOSINE TRIPHOSPHATE; ADOLESCENT; ADULT; DNA DAMAGE; DNA, MITOCHONDRIAL; FEMALE; FRIEDREICH ATAXIA; HUMANS; IRON-BINDING PROTEINS; MALE; MIDDLE AGED; MITOCHONDRIA; MUSCLE, SKELETAL; NERVE TISSUE PROTEINS; OXIDATIVE PHOSPHORYLATION; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); TRINUCLEOTIDE REPEATS;

ATAXIA;

EID: 0033613262     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.96.20.11492     Document Type: Article

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