Inhibitory effects of expanded GAA·TTC triplet repeats from intron I of the Friedreich ataxia gene on transcription and replication in vivo

Journal of Biological Chemistry

Volumn 273, Issue 23, 1998, Pages 14588-14595

  Ohshima, Keiichi ^a,e   Montermini, Laura ^a,f   Wells, Robert D ^b   Pandolfo, Massimo ^a,c,d  

^a CENTRE HOSPITALIER DE L UNIVERSITÉ DE MONTRÉAL   (Canada)

^b TEXAS A AND M HEALTH SCIENCE CENTER   (United States)

^c UNIVERSITÉ DE MONTRÉAL   (Canada)

^d MCGILL UNIVERSITY   (Canada)

^e Human Frontier Science Program

^f Medical Research Council of

Author keywords

[No Author keywords available]

Indexed keywords

LUCIFERASE; RIBONUCLEASE;

AMINO ACID SEQUENCE; ARTICLE; DNA STRUCTURE; ENZYME ACTIVITY; FRIEDREICH ATAXIA; GENE REPLICATION; GENETIC TRANSCRIPTION; GENOME; INTRON; NORTHERN BLOTTING; PLASMID; PRIORITY JOURNAL; PROTEIN ANALYSIS; REPORTER GENE; RNA PROCESSING;

ANIMALS; CLONING, MOLECULAR; COS CELLS; DNA REPLICATION; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; GENES, REPORTER; HUMANS; IRON-BINDING PROTEINS; NUCLEIC ACID CONFORMATION; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); PLASMIDS; RNA, MESSENGER; TRANSCRIPTION, GENETIC; TRANSFECTION; TRINUCLEOTIDE REPEATS;

ATAXIA;

EID: 0032486276     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.273.23.14588     Document Type: Article

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