Immunoreactive levels of α-ketoglutarate dehydrogenase subunits in Friedreich's ataxia and spinocerebellar ataxia type 1

Neurodegeneration

Volumn 5, Issue 1, 1996, Pages 27-33

  Mastrogiacomo, Frank ^a   LaMarche, Jacques ^b   Dožić, Slobodan ^c   Lindsay, Gordon ^d   Bettendorff, Lucien ^e   Robitaille, Yves ^f   Schut, Lawrence ^g   Kish, Stephen J ^a  

^a CENTRE FOR ADDICTION AND MENTAL HEALTH   (Canada)

^b CENTRE HOSPITALIER UNIVERSITAIRE DE SHERBROOKE   (Canada)

^c UNIVERSITY OF BELGRADE   (Serbia)

^d UNIVERSITY OF GLASGOW   (United Kingdom)

^e UNIVERSITY OF LIÈGE   (Belgium)

^f UNIVERSITÉ DE MONTRÉAL   (Canada)

^g UNIVERSITY OF MINNESOTA   (United States)

Author keywords

Cerebellum; Friedreich's ataxia; Olivopontocerebellar atrophy; Spinocerebellar ataxia type 1; ketoglutarate dehydrogenase complex

Indexed keywords

DIHYDROLIPOAMIDE DEHYDROGENASE; DIHYDROLIPOAMIDE SUCCINYLTRANSFERASE; OXOGLUTARATE DEHYDROGENASE; PYRUVATE DEHYDROGENASE;

ADULT; ARTICLE; CEREBELLUM CORTEX; CITRIC ACID CYCLE; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME SUBUNIT; FRIEDREICH ATAXIA; FRONTAL CORTEX; HUMAN; HUMAN TISSUE; OCCIPITAL CORTEX; OLIVOPONTOCEREBELLAR ATROPHY; PRIORITY JOURNAL; SPINOCEREBELLAR DEGENERATION;

EID: 0029985851     PISSN: 10558330     EISSN: None     Source Type: Journal    
DOI: 10.1006/neur.1996.0004     Document Type: Article

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