Leukodystrophies: a proposed classification system based on pathological changes and pathogenetic mechanisms

Acta Neuropathologica

Volumn 134, Issue 3, 2017, Pages 351-382

  van der Knaap, Marjo S ^a,b   Bugiani, Marianna ^a  

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b VU UNIVERSITY AMSTERDAM   (Netherlands)

Author keywords

Astrocytes; Axons; Leukodystrophy; Microglia; Myelin; Oligodendrocytes

Indexed keywords

CARBOXYPEPTIDASE C; MYELIN;

ALEXANDER DISEASE; ARTERY DISEASE; ASTROCYTE; ASTROCYTOPATHY; AXON; AXONAL SPHEROID; BASAL GANGLION; BRAIN ATROPHY; BRAIN CYST; BRAIN FUNCTION; CELL VACUOLE; CEREBELLUM; CEREBROVASCULAR ACCIDENT; DEMYELINATING DISEASE; DEMYELINATION; DISEASE CLASSIFICATION; GENE MUTATION; GM1 GANGLIOSIDOSIS; HEREDITARY DIFFUSE LEUKOENCEPHALOPATHY; HUMAN; HYPOMYELINATION; LEUKO AXONOPATHY; LEUKO VASCULOPATHY; LEUKODYSTROPHY; LEUKOENCEPHALOPATHY; MEGALENCEPHALIC LEUKOENCEPHALOPATHY; METACHROMATIC LEUKODYSTROPHY; MICROANGIOPATHY; MICROGLIA; MICROGLIOPATHY; MYELIN DISORDER; NERVE CELL DEGENERATION; NEUROPATHOLOGY; OLIGODENDROGLIA; PELIZAEUS MERZBACHER DISEASE; PRIORITY JOURNAL; REGULATORY MECHANISM; REVIEW; SUBCORTICAL CYST; TEAMWORK; TUMOR SPHEROID; VASCULAR DISEASE; WHITE MATTER; WHITE MATTER LESION; CLASSIFICATION; GLIA; MYELIN SHEATH; PATHOLOGY;

AXONS; DEMYELINATING DISEASES; HUMANS; MYELIN SHEATH; NEUROGLIA; WHITE MATTER;

EID: 85021054689     PISSN: 00016322     EISSN: 14320533     Source Type: Journal    
DOI: 10.1007/s00401-017-1739-1     Document Type: Review

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