Increased density of oligodendrocytes in childhood ataxia with diffuse central hypomyelination (CACH) syndrome: Neuropathological and biochemical study of two cases

Acta Neuropathologica

Volumn 97, Issue 5, 1999, Pages 469-480

  Rodriguez, D ^a   Gelot, A ^b   Della Gaspera, B ^c   Robain, O ^d   Ponsot, G ^a   Sarlieve L L ^e   Ghandour, S ^e   Pompidou, A ^b   Dautigny, A ^c   Aubourg, P ^a   Pham Dinh, D ^c  

^a HÔPITAL SAINT VINCENT DE PAUL   (France)

^b INSTITUT DE RECHERCHES INTERNATIONALES SERVIER   (France)

^c CNRS   (France)

^d Hôpital Port Royal ^*  (France)

^e UNIVERSITÉ DE STRASBOURG   (France)

Author keywords

CACH syndrome; Leukodystrophy; Myelin; Oligodendrocyte; Orthochromatic

Indexed keywords

2',3' CYCLIC NUCLEOTIDE 3' PHOSPHODIESTERASE; ANTIBODY; CARBONATE DEHYDRATASE II; GLIAL FIBRILLARY ACIDIC PROTEIN; GLYCOPROTEIN; LIPID; MYELIN; MYELIN BASIC PROTEIN; MYELIN PROTEIN; PROTEOLIPID PROTEIN;

ANTERIOR COMMISSURE; ARTICLE; ATAXIA; BIOCHEMISTRY; CACH SYNDROME; CAPSULA INTERNA; CASE REPORT; CELL DENSITY; CELL POPULATION; CEREBELLUM; CHILD; CORPUS CALLOSUM; CYTOPLASM; DISEASE SEVERITY; GLIA CELL; HEMISPHERE; HUMAN; HUMAN TISSUE; INFANT; LEUKODYSTROPHY; MACROGLIA; MALE; MICROGLIA; MITOSIS RATE; MORPHOLOGY; MYELINATION; NERVE FIBER; NEUROPATHOLOGY; NEWBORN; OLIGODENDROGLIA; PRIORITY JOURNAL; WHITE MATTER;

ATAXIA; BRAIN; CHILD; HUMANS; MALE; MYELIN SHEATH; OLIGODENDROGLIA; ORGAN SIZE; SYNDROME;

EID: 0032912163     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004010051016     Document Type: Article

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