GlialCAM, a Protein Defective in a Leukodystrophy, Serves as a ClC-2 Cl - Channel Auxiliary Subunit

Neuron

Volumn 73, Issue 5, 2012, Pages 951-961

  Jeworutzki, Elena ^a   López Hernández, Tania ^b   Capdevila Nortes, Xavier ^b   Sirisi, Sònia ^b,d   Bengtsson, Luiza ^c   Montolio, Marisol ^b,e   Zifarelli, Giovanni ^a   Arnedo, Tanit ^b   Müller, Catrin S ^f   Schulte, Uwe ^f   Nunes, Virginia ^b,d,e   Martínez, Albert ^b   Jentsch, Thomas J ^c   Gasull, Xavier ^b   Pusch, Michael ^a   Estévez, Raúl ^b,e  

^a CNR   (Italy)

^b UNIVERSITY OF BARCELONA   (Spain)

^c MAX DELBRÜCK CENTER FOR MOLECULAR MEDICINE   (Germany)

^d BELLVITGE BIOMEDICAL RESEARCH INSTITUTE IDIBELL   (Spain)

^e CENTRO DE INVESTIGACIÓN BIOMÉDICA EN RED DE ENFERMEDADES RARAS CIBERER   (Spain)

^f LOGOPHARM GMBH   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CELL ADHESION MOLECULE; CHLORIDE CHANNEL; CIC 2 CHLORIDE CHANNEL; GLIALCAM PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; ASTROCYTE; CELL JUNCTION; CELLULAR DISTRIBUTION; CHANNEL GATING; CHLORIDE CURRENT; CONTROLLED STUDY; GENE; GENE MUTATION; GLIA; GLIALCAM GENE; HUMAN; HUMAN CELL; HUMAN TISSUE; LEUKODYSTROPHY; MYELINATED NERVE; NONHUMAN; PRIORITY JOURNAL; PROTEIN LOCALIZATION; RAT;

ANIMALS; BIOPHYSICS; CELLS, CULTURED; CHLORIDE CHANNELS; CONNEXINS; ELECTRIC STIMULATION; GLIAL FIBRILLARY ACIDIC PROTEIN; GREEN FLUORESCENT PROTEINS; HUMANS; IMMUNOPRECIPITATION; MASS SPECTROMETRY; MEMBRANE POTENTIALS; MICE; MICE, TRANSGENIC; MICROINJECTIONS; MICROSCOPY, CONFOCAL; MICROSCOPY, ELECTRON, TRANSMISSION; MODELS, MOLECULAR; MUTATION; MYELIN SHEATH; MYOSIN LIGHT CHAINS; NEUROGLIA; OOCYTES; PATCH-CLAMP TECHNIQUES; PROTEIN TRANSPORT; RATS; TRANSFECTION; XENOPUS;

EID: 84858019171     PISSN: 08966273     EISSN: 10974199     Source Type: Journal    
DOI: 10.1016/j.neuron.2011.12.039     Document Type: Article

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