Regulation of protein synthesis in lymphoblasts from vanishing white matter patients

Neurobiology of Disease

Volumn 21, Issue 3, 2006, Pages 496-504

  Van Kollenburg, Barbara ^a   Thomas, Adri A M ^b   Vermeulen, Gerre ^a   Bertrand, Gesina A M ^a   Van Berkel, Carola G M ^a   Pronk, Jan C ^a   Proud, Christopher G ^c   Van Der Knaap, Marjo S ^a   Scheper, Gert C ^a  

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b UTRECHT UNIVERSITY   (Netherlands)

^c UNIVERSITY OF BRITISH COLUMBIA   (Canada)

Author keywords

Childhood; eIF2B; Heat shock; Leukoencephalopathy; Translation; White matter

Indexed keywords

GUANINE NUCLEOTIDE EXCHANGE FACTOR; INITIATION FACTOR 2; INITIATION FACTOR 2ALPHA; METHIONINE; PROTEIN; PROTEIN SUBUNIT; SULFUR 35;

ARTICLE; COMPARATIVE STUDY; CONTROLLED STUDY; HEAT SHOCK; HUMAN; HUMAN CELL; LYMPHOBLAST; MUTATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; PROTEIN SYNTHESIS; REGULATORY MECHANISM; THERMAL EXPOSURE; WESTERN BLOTTING; WHITE MATTER;

BLOTTING, WESTERN; BRAIN DISEASES; CELLS, CULTURED; EUKARYOTIC INITIATION FACTOR-2; FEVER; HEAT; HEAT-SHOCK PROTEINS; HUMANS; LYMPHOCYTES; MUTATION; PHOSPHORYLATION;

EID: 33244482231     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2005.08.009     Document Type: Article

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