Mice with megalencephalic leukoencephalopathy with cysts: A developmental angle

Annals of Neurology

Volumn 77, Issue 1, 2015, Pages 114-131

  Dubey, Mohit ^a,b   Bugiani, Marianna ^a   Ridder, Margreet C ^a   Postma, Nienke L ^a   Brouwers, Eelke ^a,b   Polder, Emiel ^a   Gerbren Jacobs, J ^a,b   Baayen, Johannes C ^a   Klooster, Jan ^c   Kamermans, Maarten ^c   Aardse, Romy ^b   De Kock, Christiaan P J ^b   Dekker, Marien P ^b   Van Weering, Jan R T ^b   Heine, Vivi M ^a,b   Abbink, Truus E M ^a   Scheper, Gert C ^a   Boor, Ilja ^a   Lodder, Johannes C ^b   Mansvelder, Huibert D ^b   Van Der Knaap, Marjo S ^a,b   more..

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b VU UNIVERSITY AMSTERDAM   (Netherlands)

^c NETHERLANDS INSTITUTE FOR NEUROSCIENCE   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CELL ADHESION MOLECULE; CHLORIDE CHANNEL; CHLORIDE CHANNEL 2; HYPOTONIC SOLUTION; MLC1 PROTEIN; MYELIN BASIC PROTEIN; PROTEIN; RNA; TAMOXIFEN; UNCLASSIFIED DRUG; MEMBRANE PROTEIN; MLC1 PROTEIN, MOUSE; PROTEIN S100B; S100B PROTEIN, HUMAN;

ADOLESCENT; ADULT; ALEXANDER DISEASE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTE; ASTROCYTE CULTURE; BRAIN CELL; BRAIN CYST; BRAIN WATER; BRAIN WEIGHT; CELL DENSITY; CELL STRUCTURE; CELL VACUOLE; CHILD; CONTROLLED STUDY; ELECTRON MICROSCOPY; ELECTROPHYSIOLOGY; EMBRYO; GENETIC DISORDER; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; IMMUNOHISTOCHEMISTRY; INFANT; LEUKOENCEPHALOPATHY; MALE; MEGALENCEPHALIC LEUKOENCEPHALOPATHY WITH CYST; MOTOR ACTIVITY; MOTOR COORDINATION; MOTOR PERFORMANCE; MOUSE; MYELINATION; NEWBORN; NONHUMAN; OPEN FIELD TEST; POLYACRYLAMIDE GEL ELECTROPHORESIS; POLYMERASE CHAIN REACTION; POTASSIUM CURRENT; PRIMARY CULTURE; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; PROTEIN STABILITY; QUANTITATIVE ANALYSIS; RNA ISOLATION; WESTERN BLOTTING; AGE; ANIMAL; BODY EQUILIBRIUM; BRAIN CORTEX; BRAIN EDEMA; C57BL MOUSE; CEREBELLUM; CYST; CYTOLOGY; DEMYELINATING DISEASE; DISEASE MODEL; GENE EXPRESSION REGULATION; GENETICS; MEMBRANE POTENTIAL; METABOLISM; PATHOLOGY; PATHOPHYSIOLOGY; PRESCHOOL CHILD; SENSORY DYSFUNCTION; TRANSGENIC MOUSE; ULTRASTRUCTURE; WHITE MATTER; YOUNG ADULT;

ADOLESCENT; ADULT; AGE FACTORS; ANIMALS; ANIMALS, NEWBORN; ASTROCYTES; BRAIN EDEMA; CEREBELLUM; CEREBRAL CORTEX; CHILD; CHILD, PRESCHOOL; CYSTS; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HEREDITARY CENTRAL NERVOUS SYSTEM DEMYELINATING DISEASES; HUMANS; INFANT; INFANT, NEWBORN; MEMBRANE POTENTIALS; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MOTOR ACTIVITY; POSTURAL BALANCE; S100 CALCIUM BINDING PROTEIN BETA SUBUNIT; SENSATION DISORDERS; WHITE MATTER; YOUNG ADULT;

EID: 84920873926     PISSN: 03645134     EISSN: 15318249     Source Type: Journal    
DOI: 10.1002/ana.24307     Document Type: Article

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