Defective glial maturation in vanishing white matter disease

Journal of Neuropathology and Experimental Neurology

Volumn 70, Issue 1, 2011, Pages 69-82

  Bugiani, Marianna ^a   Boor, Ilja ^a   Van Kollenburg, Barbara ^a   Postma, Nienke ^a   Polder, Emiel ^a   Van Berkel, Carola ^a   Van Kesteren, Ronald E ^b   Windrem, Martha S ^d   Hol, Elly M ^c   Scheper, Gert C ^a   Goldman, Steven A ^d   Van Der Knaap, Marjo S ^a  

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b VU UNIVERSITY AMSTERDAM   (Netherlands)

^c NETHERLANDS INSTITUTE FOR NEUROSCIENCE   (Netherlands)

^d UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

Author keywords

Astrocytes; GFAP ; Glia maturation; Olig2 cytoplasmic translocation; Oligodendrocyte progenitor cells; Vanishing white matter

Indexed keywords

ALPHA CRYSTALLIN; BETA CRYSTALLIN; GLIAL FIBRILLARY ACIDIC PROTEIN; HEAT SHOCK PROTEIN; ISOPROTEIN; MYELIN;

ADOLESCENT; ADULT; AGED; ARTICLE; ASTROCYTE; BRAIN DISEASE; CELL ASSAY; CELL FUNCTION; CELL MATURATION; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; GLIA; HISTOCHEMISTRY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOCYTOCHEMISTRY; INTERMEDIATE FILAMENT; OLIGODENDROGLIA; POLYMERASE CHAIN REACTION; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; STEM CELL; TISSUE GROWTH; WESTERN BLOTTING; WHITE MATTER;

ADOLESCENT; ADULT; AGED; CELL DIFFERENTIATION; CELL ENLARGEMENT; CHILD; CHILD, PRESCHOOL; HUMANS; INFANT; LEUKOENCEPHALOPATHIES; MIDDLE AGED; NERVE FIBERS, MYELINATED; NEUROGLIA; YOUNG ADULT;

EID: 78650677308     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318203ae74     Document Type: Article

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