Cardiac energetics are abnormal in Friedreich ataxia patients in the absence of cardiac dysfunction and hypertrophy: An in vivo 31P magnetic resonance spectroscopy study

Cardiovascular Research

Volumn 52, Issue 1, 2001, Pages 111-119

  Lodi, Raffaele ^a,b   Rajagopalan, Bheeshma ^a   Blamire, Andrew M ^a   Cooper, J Mark ^c   Davies, Crispin H ^d   Bradley, Jane L ^c   Styles, Peter ^a   Schapira, Anthony H V ^c,e  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b UNIVERSITY OF BOLOGNA   (Italy)

^c ROYAL FREE AND UNIVERSITY COLLEGE MEDICAL SCHOOL   (United Kingdom)

^d JOHN RADCLIFFE HOSPITAL   (United Kingdom)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

Energy metabolism; Free radicals; Hypertrophy; Mitochondria; Oxidative phosphorylation

Indexed keywords

ADENOSINE TRIPHOSPHATE; CREATINE PHOSPHATE; FRATAXIN; PHOSPHORUS;

ADOLESCENT; ADULT; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BIOENERGY; CLINICAL ARTICLE; CONTROLLED STUDY; DEATH; DISEASE ASSOCIATION; ECHOCARDIOGRAPHY; FEMALE; FRIEDREICH ATAXIA; GENE; HEART CONTRACTION; HEART DEVELOPMENT; HEART DISEASE; HEART MUSCLE METABOLISM; HEART VENTRICLE HYPERTROPHY; HUMAN; MALE; MITOCHONDRIAL RESPIRATION; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PRIORITY JOURNAL;

EID: 0034839688     PISSN: 00086363     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0008-6363(01)00357-1     Document Type: Article

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