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Biochimica et Biophysica Acta - Bioenergetics

Volumn 1504, Issue 1, 2001, Pages 20-30

What do mitochondrial diseases teach us about normal mitochondrial functions... that we already knew: Threshold expression of mitochondrial defects

(6) Mazat, Jean Pierre a Rossignol, Rodrigue a Malgat, Monique a Rocher, Christophe a Faustin, Benjamin a Letellier, Thierry a

a INSERM (France)

Author keywords

Inborn error of metabolism; Metabolic control analysis; Mitochondria; Mitochondrial diseases; Oxidative phosphorylation

Indexed keywords

ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; FREE RADICAL; MITOCHONDRIAL DNA;

ANALYTIC METHOD; CELL MEMBRANE TRANSPORT; CLINICAL FEATURE; COMPLEX FORMATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ENZYME INHIBITION; GENE MUTATION; MAXIMUM ALLOWABLE CONCENTRATION; METABOLIC REGULATION; METABOLITE; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; REVIEW; SYNTHESIS; TISSUE SPECIFICITY;

ADENOSINE TRIPHOSPHATE; ANIMALS; CELLS, CULTURED; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT COMPLEX IV; ENZYME INHIBITORS; HUMANS; MITOCHONDRIA; MITOCHONDRIAL MYOPATHIES; MUTATION; OXIDATIVE PHOSPHORYLATION; POTASSIUM CYANIDE;

EID: 0035282929 PISSN: 00052728 EISSN: None Source Type: Journal
DOI: 10.1016/S0005-2728(00)00236-X Document Type: Review

Times cited : (80)

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