Nuclear trafficking in amyotrophic lateral sclerosis and frontotemporal lobar degeneration

Brain

Volumn 140, Issue 1, 2017, Pages 13-26

  Mihevc, Sonja Prpar ^a   Darovic, Simona ^a   Kovanda, Anja ^a   Česnik, Ana Bajc ^a   Župunski, Vera ^b   Rogelj, Boris ^a,b,c  

^a JO EF STEFAN INSTITUTE   (Slovenia)

^b UNIVERSITY OF LJUBLJANA   (Slovenia)

^c Biomedical Research Institute BRIS   (Slovenia)

Author keywords

Amyotrophic lateral sclerosis; C9ORF72; Frontotemporal lobar degeneration; FUS; Nucleocytoplasmic transport; TDP 43

Indexed keywords

DIPEPTIDE; GUANINE NUCLEOTIDE EXCHANGE C9ORF72; TAR DNA BINDING PROTEIN; C9ORF72 PROTEIN, HUMAN; DNA BINDING PROTEIN; FUS PROTEIN, HUMAN; PROTEIN; RNA BINDING PROTEIN FUS; TDP-43 PROTEIN, HUMAN;

AMYOTROPHIC LATERAL SCLEROSIS; BIOACCUMULATION; C9ORF72 GENE; FRONTOTEMPORAL DEMENTIA; GENE; GENE MUTATION; HUMAN; NONHUMAN; NUCLEOCYTOPLASMIC TRANSPORT; PATHOGENESIS; PRIORITY JOURNAL; REVIEW; CELL NUCLEUS; METABOLISM;

ACTIVE TRANSPORT, CELL NUCLEUS; AMYOTROPHIC LATERAL SCLEROSIS; CELL NUCLEUS; DNA-BINDING PROTEINS; FRONTOTEMPORAL LOBAR DEGENERATION; HUMANS; PROTEINS; RNA-BINDING PROTEIN FUS;

EID: 85015606615     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/aww197     Document Type: Review

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