Abundant FUS-immunoreactive pathology in neuronal intermediate filament inclusion disease

Acta Neuropathologica

Volumn 118, Issue 5, 2009, Pages 605-616

  Neumann, Manuela ^a   Roeber, Sigrun ^b   Kretzschmar, Hans A ^b   Rademakers, Rosa ^c   Baker, Matt ^c   MacKenzie, Ian R A ^d  

^a UNIVERSITY HOSPITAL ZURICH   (Switzerland)

^b UNIVERSITY OF MUNICH   (Germany)

^c MAYO CLINIC   (United States)

^d VANCOUVER GENERAL HOSPITAL   (Canada)

Author keywords

Frontotemporal dementia; Frontotemporal lobar degeneration; Fused in sarcoma; Neuronal intermediate filament disease; Translocated in liposarcoma

Indexed keywords

ALPHA INTERNEXIN; CELL PROTEIN; DNA; FUSED IN SARCOMA PROTEIN; INTERMEDIATE FILAMENT PROTEIN; NEUROFILAMENT HEAVY SUBUNIT; NEUROFILAMENT LIGHT SUBUNIT; NEUROFILAMENT M PROTEIN; NEUROFILAMENT PROTEIN; UNCLASSIFIED DRUG;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; BRAIN TISSUE; CELL NUCLEUS INCLUSION BODY; CELLULAR DISTRIBUTION; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOPLASM; DEGENERATIVE DISEASE; EXTRAPYRAMIDAL SYMPTOM; FEMALE; FRONTOTEMPORAL DEMENTIA; GENE MUTATION; HUMAN; HUMAN TISSUE; IMMUNOFLUORESCENCE TEST; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; MALE; MUTATIONAL ANALYSIS; NEURONAL INTERMEDIATE FILAMENT INCLUSION DISEASE; NEUROPATHOLOGY; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN FUNCTION; PYRAMIDAL SIGN;

ADULT; AGED; CARRIER PROTEINS; CELL CYCLE PROTEINS; CYTOMEGALOVIRUS INFECTIONS; DNA MUTATIONAL ANALYSIS; FEMALE; HUMANS; INTERMEDIATE FILAMENTS; INTRANUCLEAR INCLUSION BODIES; MALE; MIDDLE AGED; NEURONS; RNA, MESSENGER; RNA-BINDING PROTEIN FUS;

EID: 70449521091     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-009-0581-5     Document Type: Article

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