Pathways to mitochondrial dysfunction in ALS pathogenesis

Biochemical and Biophysical Research Communications

Volumn 483, Issue 4, 2017, Pages 1187-1193

  Carrì, Maria Teresa ^a,b   D'Ambrosi, Nadia ^c   Cozzolino, Mauro ^d  

^a UNIVERSITY OF ROME TOR VERGATA   (Italy)

^b IRCCS FONDAZIONE SANTA LUCIA   (Italy)

^c CATHOLIC UNIVERSITY   (Italy)

^d INSTITUTE OF TRANSLATIONAL PHARMACOLOGY   (Italy)

Author keywords

Alternative splicing; Amyotrophic Lateral Sclerosis; Mitochondria; Mitophagy; Protein aggregation

Indexed keywords

C9ORF72 PROTEIN; CELL MEMBRANE PROTEIN; CHCHD10 PROTEIN; COPPER ZINC SUPEROXIDE DISMUTASE; OPTINEURIN; PHOSPHOTRANSFERASE; RNA BINDING PROTEIN FUS; SEQUESTOSOME 1; SIGMA1R PROTEIN; SYNAPTOBREVIN; TANK BINDING KINASE; TAR DNA BINDING PROTEIN; UNCLASSIFIED DRUG; VESICLE ASSOCIATED MEMBRANE PROTEIN ASSOCIATED PROTEIN B; VESICLE ASSOCIATED MEMBRANE PROTEIN ASSOCIATED PROTEIN C;

AMYOTROPHIC LATERAL SCLEROSIS; AUTOPHAGY; CELL INTERACTION; CELL STRUCTURE; CLEARANCE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENDOPLASMIC RETICULUM; GENE MUTATION; HUMAN; MITOCHONDRIAL MEMBRANE; MITOCHONDRION; MOLECULAR PATHOLOGY; NONHUMAN; PRIORITY JOURNAL; PROTEIN FUNCTION; REVIEW; RNA PROCESSING; SIGNAL TRANSDUCTION; ANIMAL; GENETICS; METABOLISM; MUTATION; PATHOPHYSIOLOGY; PHYSIOLOGY;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; HUMANS; MITOCHONDRIA; MUTATION;

EID: 85002697091     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2016.07.055     Document Type: Review

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