Mechanisms of toxicity in C9FTLD/ALS

Acta Neuropathologica

Volumn 127, Issue 3, 2014, Pages 359-376

  Gendron, Tania F ^a   Belzil, Veronique V ^a   Zhang, Yong Jie ^a   Petrucelli, Leonard ^a  

^a MAYO CLINIC   (United States)

Author keywords

Amyotrophic lateral sclerosis; Bidirectional transcription; C9ORF72; Epigenetics; Expanded repeat; Frontotemporal lobar degeneration; Repeat associated non ATG translation; RNA foci

Indexed keywords

ANTISENSE OLIGODEOXYNUCLEOTIDE; HETEROGENEOUS NUCLEAR RIBONUCLEOPROTEIN A3; MESSENGER RNA; RNA BINDING PROTEIN; UNCLASSIFIED DRUG;

AMYOTROPHIC LATERAL SCLEROSIS; CYTOTOXICITY; EPIGENETICS; FRONTOTEMPORAL DEMENTIA; GC RICH SEQUENCE; GENE EXPRESSION; HUMAN; LOSS OF FUNCTION MUTATION; MYOTONIC DYSTROPHY; NEUROPATHOLOGY; NEUROTOXICITY; NONHUMAN; NUCLEOTIDE REPEAT; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN INTERACTION; REVIEW; TRANSCRIPTION REGULATION; TRANSLATION INITIATION;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; BRAIN; DNA REPEAT EXPANSION; FRONTOTEMPORAL LOBAR DEGENERATION; HUMANS; NEURODEGENERATIVE DISEASES; PROTEINS; RNA; SPINAL CORD;

EID: 84896699383     PISSN: 00016322     EISSN: 14320533     Source Type: Journal    
DOI: 10.1007/s00401-013-1237-z     Document Type: Review

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