SOD1 misplacing and mitochondrial dysfunction in amyotrophic lateral sclerosis pathogenesis

Frontiers in Cellular Neuroscience

Volumn 9, Issue AUGUST, 2015, Pages

  Tafuri, Francesco ^a   Ronchi, Dario ^a   Magri, Francesca ^a   Comi, Giacomo P ^a   Corti, Stefania ^a  

^a UNIVERSITY OF MILAN   (Italy)

Author keywords

Mitochondria; Mitochondrial intermembrane space; Motor neuron disorder; Outer mitochondrial membrane; Protein misfolding; Superoxide dismutase 1

Indexed keywords

CHAPERONE; COPPER ZINC SUPEROXIDE DISMUTASE; CYSTEINE; CYTOCHROME C OXIDASE; MANGANESE SUPEROXIDE DISMUTASE; PROTEIN BCL 2; TAR DNA BINDING PROTEIN; VOLTAGE DEPENDENT ANION CHANNEL 2; VOLTAGE DEPENDENT ANION CHANNEL 3;

AMYOTROPHIC LATERAL SCLEROSIS; DEGENERATIVE DISEASE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; GENE MUTATION; MITOCHONDRIAL DYSFUNCTION; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL TOXICITY; NONHUMAN; PATHOGENESIS; PHENOTYPE; PROTEIN LOCALIZATION; REVIEW;

EID: 84941007556     PISSN: 16625102     EISSN: None     Source Type: Journal    
DOI: 10.3389/fncel.2015.00336     Document Type: Review

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