Copper-Zinc Superoxide Dismutase, Its Copper Chaperone, and Familial Amyotrophic Lateral Sclerosis

Protein Misfolding Diseases: Current and Emerging Principles and Therapies

Volumn , Issue , 2010, Pages 381-401

  Winkler, Duane D ^a   Prudencio, Mercedes ^b   Karch, Celeste ^c   Borchelt, David R ^b   Hart, P John ^a  

^a University of Texas Health Science Center   (United States)

^b UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^c WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Copper chaperone for SOD1 and SOD1 maturation; Copper zinc superoxide dismutase, its copper chaperone and familial amyotrophic lateral sclerosis; Immature pathogenic SOD1 and toxicity

Indexed keywords

EID: 84886134329     PISSN: None     EISSN: None     Source Type: Book    
DOI: 10.1002/9780470572702.ch17     Document Type: Chapter

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