Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

Brain

Volumn 129, Issue 2, 2006, Pages 451-464

  Jonsson, P Andreas ^a   Graffmo, Karin S ^a   Andersen, Peter M ^a   Brännström, Thomas ^a   Lindberg, Mikael ^a   Oliveberg, Mikael ^b   Marklund, Stefan L ^a  

^a UMEÅ UNIVERSITY   (Sweden)

^b STOCKHOLM UNIVERSITY   (Sweden)

Author keywords

Aggregates; Amyotrophic lateral sclerosis; Disulphide bond; Misfolding; Superoxide dismutase

Indexed keywords

COPPER; COPPER ZINC SUPEROXIDE DISMUTASE; MUTANT PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CENTRAL NERVOUS SYSTEM; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; CYTOTOXICITY; DISULFIDE BOND; ENZYME ACTIVITY; ENZYME LOCALIZATION; ENZYME STRUCTURE; ENZYME SYNTHESIS; FRACTIONATION; HISTOPATHOLOGY; HUMAN; LIFESPAN; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FOLDING; SPINAL CORD; STEADY STATE; TISSUE DISTRIBUTION; TRANSGENIC MOUSE; WILD TYPE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CENTRAL NERVOUS SYSTEM; COPPER; DISULFIDES; HUMANS; MICE; MICE, TRANSGENIC; MODELS, ANIMAL; MOLECULAR CHAPERONES; MOTOR NEURONS; PROTEIN CONFORMATION; SUPEROXIDE DISMUTASE;

EID: 31544467869     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/awh704     Document Type: Article

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