Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

Neurobiology of Disease

Volumn 10, Issue 2, 2002, Pages 128-138

  Wang, Jiou ^a   Xu, Guilian ^a   Gonzales, Victoria ^a   Coonfield, Michael ^a   Fromholt, David ^a   Copeland, Neal G ^b   Jenkins, Nancy A ^b   Borchelt, David R ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b NATIONAL CANCER INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ION; COPPER ZINC SUPEROXIDE DISMUTASE; HISTIDINE; MUTANT PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BINDING SITE; CELL INCLUSION; CONTROLLED STUDY; EMBRYO; GENE MUTATION; METAL BINDING; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NERVE CELL DEGENERATION; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; TRANSGENIC MOUSE;

EID: 0036076642     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1006/nbdi.2002.0498     Document Type: Article

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