Structural properties and neuronal toxicity of amyotrophic lateral sclerosis-associated Cu/Zn superoxide dismutase 1 aggregates

Journal of Cell Biology

Volumn 171, Issue 1, 2005, Pages 75-85

  Matsumoto, Gen ^a   Stojanovic, Aleksandar ^a   Holmberg, Carina I ^a   Kim, Soojin ^a   Morimoto, Richard I ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; HEAT SHOCK PROTEIN 70; MUTANT PROTEIN; PROTEASOME;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; ENZYME STRUCTURE; ENZYME SUBSTRATE; IMAGING; MICROSCOPY; NERVE CELL; NERVE CELL NECROSIS; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION; RAT; STRUCTURE ANALYSIS;

AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; CELL DEATH; CELLS, CULTURED; HELA CELLS; HSP70 HEAT-SHOCK PROTEINS; HUMANS; MACROMOLECULAR SUBSTANCES; MUTATION; NEURONS; PC12 CELLS; PROTEASOME ENDOPEPTIDASE COMPLEX; PROTEIN CONFORMATION; PROTEIN FOLDING; RATS; SUPEROXIDE DISMUTASE;

EID: 26444471905     PISSN: 00219525     EISSN: 00219525     Source Type: Journal    
DOI: 10.1083/jcb.200504050     Document Type: Article

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