Structural consequences of the familial amyotrophic lateral sclerosis SOD1 mutant His46Arg

Protein Science

Volumn 14, Issue 5, 2005, Pages 1201-1213

  Antonyuk, Svetlana ^a   Elam, Jennifer Stine ^b   Hough, Michael A ^a   Strange, Richard W ^a   Doucette, Peter A ^c   Rodriguez, Jorge A ^c   Hayward, Lawrence J ^d   Valentine, Joan Selverstone ^c   Hart, P John ^b   Hasnain, S Samar ^a  

^a DARESBURY LABORATORY   (United Kingdom)

^b UNIVERSITY OF TEXAS HEALTH SCIENCE CENTER AT SAN ANTONIO   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

^d UNIVERSITY OF MASSACHUSETTS MEDICAL SCHOOL   (United States)

Author keywords

ALS; Amyloid; Copper zinc superoxide dismutase; Familial amyotrophic lateral sclerosis; H46R; SOD1

Indexed keywords

ARGININE; COPPER ZINC SUPEROXIDE DISMUTASE; HISTIDINE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ARTICLE; BINDING SITE; CONTROLLED STUDY; CRYSTAL STRUCTURE; FAMILIAL DISEASE; HUMAN; HUMAN CELL; METAL BINDING; MOTONEURON; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; RAT; TRANSGENIC ANIMAL;

AMYOTROPHIC LATERAL SCLEROSIS; ARGININE; HISTIDINE; HUMANS; MODELS, MOLECULAR; POINT MUTATION; PROTEIN CONFORMATION; SUPEROXIDE DISMUTASE; ZINC;

EID: 20244386847     PISSN: 09618368     EISSN: None     Source Type: Journal    
DOI: 10.1110/ps.041256705     Document Type: Article

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