Minute quantities of misfolded mutant superoxide dismutase-1 cause amyotrophic lateral sclerosis

Brain

Volumn 127, Issue 1, 2004, Pages 73-88

  Jonsson, P Andreas ^a   Ernhill, Karin ^a   Andersen, Peter M ^a   Bergemalm, Daniel ^a   Brännström, Thomas ^a   Gredal, Ole ^c   Nilsson, Peter ^a,b   Marklund, Stefan L ^a,d  

^a UMEÅ UNIVERSITY HOSPITAL   (Sweden)

^b HALMSTAD HOSPITAL   (Sweden)

^c BISPEBJERG HOSPITAL   (Denmark)

^d UMEÅ UNIVERSITY   (Sweden)

Author keywords

Aggregation; Motor neuron disease; SOD; Transgenic mice

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; DETERGENT; EPITOPE; MUTANT PROTEIN; SUPEROXIDE DISMUTASE; UNCLASSIFIED DRUG;

ADULT; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTE; BRAIN; CASE REPORT; CELL DAMAGE; CONTROLLED STUDY; DISEASE MARKER; ENZYME ACTIVITY; FEMALE; HUMAN; HUMAN TISSUE; ISOELECTRIC FOCUSING; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; PROTEIN MISFOLDING; SPINAL CORD; SPINAL CORD VENTRAL HORN; STEADY STATE; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; ANTERIOR HORN CELLS; BRAIN; DETERGENTS; DISEASE MODELS, ANIMAL; FEMALE; HUMANS; MICE; MICE, TRANSGENIC; MIDDLE AGED; MUTATION; PHENOTYPE; SOLUBILITY; SPINAL CORD; SUPEROXIDE DISMUTASE; SURVIVAL ANALYSIS;

EID: 0347358915     PISSN: 00068950     EISSN: None     Source Type: Journal    
DOI: 10.1093/brain/awh005     Document Type: Article

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