Endogenous and synthetic neurosteroids in treatment of Niemann-Pick Type C disease

Brain Research Reviews

Volumn 57, Issue 2, 2008, Pages 410-420

  Mellon, Synthia H ^a   Gong, Wenhui ^a   Schonemann, Marcus D ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Allopregnanolone; GABAA receptor; Niemann Pick type C; Pregnane X receptor

Indexed keywords

3(OR 17)BETA HYDROXYSTEROID DEHYDROGENASE; 3ALPHA HYDROXY 5ALPHA PREGNAN 20 ONE; 3ALPHA HYDROXYSTEROID DEHYDROGENASE; 4 AMINOBUTYRIC ACID A RECEPTOR; BICUCULLINE; BIOCHEMICAL MARKER; CHOLESTEROL; CHOLESTEROL MONOOXYGENASE (SIDE CHAIN CLEAVING); GANAXOLONE; GANGLIOSIDE; GLYCOLIPID; NEUROSTEROID; PREGNANE X RECEPTOR; STEROID 5ALPHA REDUCTASE;

ATAXIA; AUTOSOMAL RECESSIVE DISORDER; CELL SURVIVAL; DEGENERATIVE DISEASE; DOSE RESPONSE; DRUG EFFECT; DRUG MECHANISM; GENE MUTATION; GRANULE CELL; LOCOMOTION; LYSOSOME; MOTOR COORDINATION; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; PURKINJE CELL; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; REVIEW; SINGLE DRUG DOSE; SURVIVAL TIME; TREMOR; WEIGHT REDUCTION;

ANIMALS; DISEASE MODELS, ANIMAL; GONADAL STEROID HORMONES; HUMANS; MICE; NIEMANN-PICK DISEASE, TYPE C; PREGNANOLONE; RECEPTORS, GABA-A;

EID: 40749148475     PISSN: 01650173     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.brainresrev.2007.05.012     Document Type: Review

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