Neurons in Niemann-Pick disease type C accumulate gangliosides as well as unesterified cholesterol and undergo dendritic and axonal alterations

Journal of Neuropathology and Experimental Neurology

Volumn 60, Issue 1, 2001, Pages 49-64

  Zervas, Mark ^a   Dobrenis, Kostantin ^a   Walkley, Steven U ^a  

^a ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

Axonal Spheroid; Dendrite; Endosome; Ganglioside; Lysosome; Meganeurite; Unesterified cholesterol

Indexed keywords

CHOLESTEROL; FILIPIN; GANGLIOSIDE; GANGLIOSIDE GD2; GANGLIOSIDE GD3; GANGLIOSIDE GM1; GANGLIOSIDE GM2; GANGLIOSIDE GM3; LYSOSOMAL ASSOCIATED MEMBRANE PROTEIN 1 ANTIBODY; LYSOSOME ASSOCIATED MEMBRANE PROTEIN 1; MEMBRANE PROTEIN; PARVALBUMIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; CEREBELLUM; CONTROLLED STUDY; DENDRITE; ENDOSOME; FERRET; GOLGI STAIN; HIPPOCAMPUS; HUMAN; IMMUNOCYTOCHEMISTRY; KUPFFER CELL; LIPID STORAGE; LYSOSOME; MOUSE; NEURITE; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; PYRAMIDAL NERVE CELL; TISSUE DISTRIBUTION;

EID: 0035142802     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1093/jnen/60.1.49     Document Type: Article

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