Bioenergetics in glutaryl-coenzyme A dehydrogenase deficiency: A role for glutaryl-coenzyme A

Journal of Biological Chemistry

Volumn 280, Issue 23, 2005, Pages 21830-21836

  Sauer, Sven W ^a   Okun, Jürgen G ^a   Schwab, Marina A ^a   Crnic, Linda R ^b   Hoffmann, Georg F ^a   Goodman, Stephen I ^b   Koeller, David M ^c   Kölker, Stefan ^a,d  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

^b UNIVERSITY OF COLORADO   (United States)

^c OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^d Division of Inborn Metabolic Diseases   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CELLS; DISEASES; FATTY ACIDS; LIVING SYSTEMS STUDIES; PATIENT MONITORING; RESPIRATORY THERAPY; TISSUE;

3-HYDROXYGLUTARIC ACIDS; ENCEPHALOPATHIC CRISIS; EXCITOTOXIC CELLS;

ENZYMES;

ACYLCARNITINE; GLUTARIC ACID; GLUTARYL COENZYME A DEHYDROGENASE; GLUTATHIONE; OXOGLUTARATE DEHYDROGENASE;

ALZHEIMER DISEASE; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; BIOENERGY; CITRIC ACID CYCLE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME INHIBITION; ENZYME PURIFICATION; FATTY ACID OXIDATION; HUNTINGTON CHOREA; MOUSE; NONHUMAN; PARKINSON DISEASE; PRIORITY JOURNAL; RESPIRATORY CHAIN; TISSUE HOMOGENATE; WILD TYPE;

ACONITATE HYDRATASE; ANIMALS; BRAIN; CATTLE; CITRIC ACID CYCLE; DIHYDROLIPOAMIDE DEHYDROGENASE; DOSE-RESPONSE RELATIONSHIP, DRUG; FATTY ACIDS; GLUTARYL-COA DEHYDROGENASE; GLUTATHIONE; ISOCITRATE DEHYDROGENASE; KETOGLUTARATE DEHYDROGENASE COMPLEX; KETONE OXIDOREDUCTASES; KINETICS; LIVER; MICE; MICE, TRANSGENIC; MYOCARDIUM; NEURODEGENERATIVE DISEASES; NEURONS; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; OXYGEN; SPECTROPHOTOMETRY;

EID: 20444466104     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M502845200     Document Type: Article

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