On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1

Journal of Neuroscience Research

Volumn 77, Issue 1, 2004, Pages 143-147

  Lund, T M ^a   Christensen, E ^b   Kristensen, A S ^a   Schousboe, A ^a   Lund, A M ^b  

^a UNIVERSITY OF COPENHAGEN   (Denmark)

^b Rigshospitalet   (Denmark)

Author keywords

Excitotoxicity; Glutaryl CoA dehydrogenase deficiency; NMDA receptor

Indexed keywords

3 HYDROXYGLUTARIC ACID; 3 METHYLGLUTACONIC ACID; DEXTRO ASPARTIC ACID; GLUTACONIC ACID; GLUTARIC ACID; GLUTARYL COENZYME A DEHYDROGENASE; N METHYL DEXTRO ASPARTIC ACID RECEPTOR; NEUROTOXIN; TRITIUM; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; AUTOSOMAL RECESSIVE INHERITANCE; CELL VIABILITY; ENZYME DEFICIENCY; FETUS; GLUTARIC ACIDEMIA TYPE 1; METABOLITE; MOUSE; NEOCORTEX; NERVE CELL CULTURE; NEUROTOXICITY; NONHUMAN; OOCYTE; PRIORITY JOURNAL; XENOPUS;

ANIMALS; BRAIN DISEASES, METABOLIC, INBORN; CELL DEATH; CELLS, CULTURED; CEREBRAL CORTEX; CORPUS STRIATUM; FETUS; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; MEMBRANE POTENTIALS; MICE; NERVE DEGENERATION; NEURONS; NEUROTOXINS; OOCYTES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; RATS; RECEPTORS, N-METHYL-D-ASPARTATE; XENOPUS;

EID: 3042805002     PISSN: 03604012     EISSN: None     Source Type: Journal    
DOI: 10.1002/jnr.20136     Document Type: Article

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